An unusual presentation of immunoglobulin A gammopathy in a patient with Schnitzler's syndrome

Elizabeth Kaganov; Divita Jhaveri; Peter Peters; Jacob W. IJdo

doi:10.1111/1756-185X.14718

An unusual presentation of immunoglobulin A gammopathy in a patient with Schnitzler's syndrome

Elizabeth Kaganov, Divita Jhaveri, Peter Peters, Jacob W. IJdo

Research output: Contribution to journal › Article › peer-review

Abstract

This case summarizes a 69-year-old woman who presented with a history of recurrent fevers, widespread urticarial rash and generalized myalgias for several years with an eventual diagnosis of Schnitzler's syndrome. This is a rare autoinflammatory condition which typically involves a chronic urticarial rash, monoclonal immunoglobulin M (IgM) or IgG gammopathy. Rapid improvement in above symptoms were noted with anakinra, an interleukin-1 receptor antagonist. We report an unusual case of a 69-year-old woman who presented with an isolated IgA monoclonal gammopathy.

Original language	English (US)
Pages (from-to)	2085-2088
Number of pages	4
Journal	International Journal of Rheumatic Diseases
Volume	26
Issue number	10
DOIs	https://doi.org/10.1111/1756-185X.14718
State	Published - Oct 2023
Externally published	Yes

Bibliographical note

Publisher Copyright:
© 2023 The Authors. International Journal of Rheumatic Diseases published by Asia Pacific League of Associations for Rheumatology and John Wiley & Sons Australia, Ltd.

Keywords

IL-1 receptor antagonist
IgA gammopathy
Schnitzler's syndrome
Schnitzler-like syndromes
anakinra

PubMed: MeSH publication types

Case Reports

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

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An unusual presentation of immunoglobulin A gammopathy in a patient with Schnitzler's syndrome

Abstract

Bibliographical note

Keywords

PubMed: MeSH publication types

UN SDGs

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