Audiological management of Cogan's syndrome

Cogan's syndrome (CS) is a rare immune-mediated disorder resulting in sensorineural hearing loss, ocular symptoms, and other systemic symptoms. This article prepares the audiologist to evaluate and treat the hearing loss seen in patients with CS. Previously published research in the medical literature is reviewed. Results of a retrospective chart review are presented along with four representative case studies. These serve to illustrate the variability of audiometric configurations and treatment options, which include corticosteroids, hearing aids, and cochlear implants. Audiologists play a pivotal role in the patient's medical team, which may include neuro-otologists, ophthalmologists, internists, rheumatologists, and other professionals as needed. It is especially important for audiologists to recognize the signs of CS and make prompt recommendations for medical intervention.